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XExtension Codes
Histopathology
Nerve sheath tumours
Nerve sheath tumours, malignant

XH3W53 category

MPNST with perineurial differentiation

Also indexed as

MPNST with perineurial differentiation

Nearby in Nerve sheath tumours, malignant

XH2XP8Malignant peripheral nerve sheath tumour
XH5C30Melanotic MPNST
XH3NT0Melanotic psammomatous MPNST
XH8HF5MPNST with glandular differentiation
XH7HR8MPNST with mesenchymal differentiation
XH4V81Malignant peripheral nerve sheath tumour, epithelioid
XH88C2Neurilemoma, malignant
XH2VV8Malignant peripheral nerve sheath tumour with rhabdomyoblastic differentiation

PreviousXH7HR8 — MPNST with mesenchymal differentiation NextXH4V81 — Malignant peripheral nerve sheath tumour, epithelioid

Browse ICD-11

01Certain infectious or parasitic diseases
02Neoplasms
03Diseases of the blood or blood-forming organs
04Diseases of the immune system
05Endocrine, nutritional or metabolic diseases
06Mental, behavioural or neurodevelopmental disorders
07Sleep-wake disorders
08Diseases of the nervous system
09Diseases of the visual system
10Diseases of the ear or mastoid process
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13Diseases of the digestive system
14Diseases of the skin
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16Diseases of the genitourinary system
17Conditions related to sexual health
18Pregnancy, childbirth or the puerperium
19Certain conditions originating in the perinatal period
20Developmental anomalies
21Symptoms, signs or clinical findings, not elsewhere classified
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23External causes of morbidity or mortality
24Factors influencing health status or contact with health services
25Codes for special purposes
26Supplementary Chapter Traditional Medicine Conditions
VSupplementary section for functioning assessment
XExtension Codes
Temporality
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Topology Scale Value
Anatomy and topography
Histopathology
Dimensions of injury
Dimensions of external causes
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5 more
Miscellaneous tumours
Mucoepidermoid neoplasms
Myomatous neoplasms
Myxomatous neoplasms
Nerve sheath tumours
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Osseous and chondromatous neoplasms
41 more
Nerve sheath tumours, benign
Nerve sheath tumours, malignant
Nerve sheath tumours, uncertain whether benign or malignant
XH2XP8Malignant peripheral nerve sheath tumour
XH5C30Melanotic MPNST
XH3NT0Melanotic psammomatous MPNST
XH8HF5MPNST with glandular differentiation
XH7HR8MPNST with mesenchymal differentiation
XH3W53MPNST with perineurial differentiation
XH4V81Malignant peripheral nerve sheath tumour, epithelioid
XH88C2Neurilemoma, malignant
XH2VV8Malignant peripheral nerve sheath tumour with rhabdomyoblastic differentiation
XH31C8Perineurioma, malignant

International Classification of Diseases, Eleventh Revision (ICD-11), World Health Organization (WHO) 2019/2021, https://icd.who.int/browse11. Licensed under Creative Commons Attribution-NoDerivatives 3.0 IGO (CC BY-ND 3.0 IGO).

Release 2026-01. View this entity in the official WHO ICD-11 browser.

This page reproduces WHO classification content for reference. It is not medical advice and must not be used to diagnose or treat. For coding decisions, consult the official release and your national coding guidelines.

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