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Histopathology
Mast cell tumours
Mast cell tumours, malignant

XH1VJ3 category

Erdheim-Chester disease

Also indexed as

Erdheim-Chester disease

Nearby in Mast cell tumours, malignant

XH6A72Mast cell sarcoma
XH2992Malignant mastocytosis
XH10N1Aggressive systemic mastocytosis
XH1H01Systemic mastocytosis with AHNMD
XH5191Systemic mastocytosis with associated haematological clonal non-mast cell disorder
XH5ER6Mast cell leukaemia

PreviousXH5ER6 — Mast cell leukaemia

Browse ICD-11

01Certain infectious or parasitic diseases
02Neoplasms
03Diseases of the blood or blood-forming organs
04Diseases of the immune system
05Endocrine, nutritional or metabolic diseases
06Mental, behavioural or neurodevelopmental disorders
07Sleep-wake disorders
08Diseases of the nervous system
09Diseases of the visual system
10Diseases of the ear or mastoid process
11Diseases of the circulatory system
12Diseases of the respiratory system
13Diseases of the digestive system
14Diseases of the skin
15Diseases of the musculoskeletal system or connective tissue
16Diseases of the genitourinary system
17Conditions related to sexual health
18Pregnancy, childbirth or the puerperium
19Certain conditions originating in the perinatal period
20Developmental anomalies
21Symptoms, signs or clinical findings, not elsewhere classified
22Injury, poisoning or certain other consequences of external causes
23External causes of morbidity or mortality
24Factors influencing health status or contact with health services
25Codes for special purposes
26Supplementary Chapter Traditional Medicine Conditions
VSupplementary section for functioning assessment
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Temporality
Aetiology
Topology Scale Value
Anatomy and topography
Histopathology
Dimensions of injury
Dimensions of external causes
Consciousness
Substances
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Other haematologic disorders
Chronic myeloproliferative disorders
Leukaemias
Hodgkin and non-Hodgkin lymphomas
Immunoproliferative diseases
Plasma cell tumours
Mast cell tumours
Neoplasms of histiocytes and accessory lymphoid cells
Histopathology by behaviour
41 more
Mast cell tumours, malignant
Mast cell tumours, uncertain whether benign or malignant
XH6A72Mast cell sarcoma
XH2992Malignant mastocytosis
XH10N1Aggressive systemic mastocytosis
XH1H01Systemic mastocytosis with AHNMD
XH5191Systemic mastocytosis with associated haematological clonal non-mast cell disorder
XH5ER6Mast cell leukaemia
XH1VJ3Erdheim-Chester disease

International Classification of Diseases, Eleventh Revision (ICD-11), World Health Organization (WHO) 2019/2021, https://icd.who.int/browse11. Licensed under Creative Commons Attribution-NoDerivatives 3.0 IGO (CC BY-ND 3.0 IGO).

Release 2026-01. View this entity in the official WHO ICD-11 browser.

This page reproduces WHO classification content for reference. It is not medical advice and must not be used to diagnose or treat. For coding decisions, consult the official release and your national coding guidelines.

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