20Developmental anomalies Multiple developmental anomalies or syndromes LD2FSyndromes with multiple structural anomalies, without predominant body system involvement LD2F.1Syndromes with multiple structural anomalies, not of environmental origin
LD2F.14
category
MURCS association
Definition MURCS association, which stands for Müllerian duct aplasia (MU), congenital renal dysplasia (R), cervical somite anomalies (CS), is the atypical (or type II) form of Mayer-Rokitansky-Küster-Hauser syndrome, characterised by utero-vaginal atresia in otherwise normal females as well associated kidney and skeletal abnormalities and hearing problems.
Also indexed as
Klippel-Feil deformity - conductive deafness - absent vagina MRKH syndrome type 2 MURCS association Mayer-Rokitansky-Küster-Hauser syndrome type 2 Müllerian aplasia - renal aplasia - cervicothoracic somite dysplasia Müllerian aplasia - renal aplasia - cervicothoracic somite dysplasia
Nearby in Syndromes with multiple structural anomalies, not of environmental origin
International Classification of Diseases, Eleventh Revision (ICD-11), World Health Organization (WHO) 2019/2021, https://icd.who.int/browse11. Licensed under Creative Commons Attribution-NoDerivatives 3.0 IGO (CC BY-ND 3.0 IGO).
Release 2026-01.
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This page reproduces WHO classification content for reference. It is not
medical advice and must not be used to diagnose or treat. For coding
decisions, consult the official release and your national coding guidelines.
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