Congenital pulmonary venous stenosis or hypoplasia
Definition
A congenital cardiovascular malformation with a pathologic narrowing of one or more pulmonary veins including diffuse hypoplasia, long segment focal/tubular stenosis and/or discrete stenosis.
Also indexed as
Congenital hypoplasia of pulmonary veinCongenital pulmonary venous hypoplasiaCongenital pulmonary venous stenosisCongenital pulmonary venous stenosis or hypoplasiaCongenital stenosis of pulmonary veincongenital pulmonary vein stenosis or hypoplasia