LA75.4
category
Congenital pulmonary airway malformations
Definition
A disease caused by failure of the bronchial structure to correctly develop during the antenatal period. This disease may present with severe respiratory distress in the newborn period, acute respiratory distress or infection later in life, or may be asymptomatic. This disease can be distinguished from other lesions and normal lung by polypoid projections of the mucosa, an increase in smooth muscle and elastic tissue within the cyst walls, an absence of cartilage in the cystic parenchyma, mucous secreting cells, and the absence of inflammation.
Inclusions
- Congenital honeycomb lung
- Congenital polycystic disease of lung
Exclusions
Also indexed as
CCAM - [Congenital cystic adenomatoid malformation]CPAM type 0 - [Congenital pulmonary airway malformation type 0]CPAM type 1 - [Congenital pulmonary airway malformation type 1]CPAM type 2 - [Congenital pulmonary airway malformation type 2]CPAM type 3 - [Congenital pulmonary airway malformation type 3]CPAM type 4 - [Congenital pulmonary airway malformation type 4]Congenital cystic adenomatoid malformationCongenital cystic disease of lungCongenital cystic lungCongenital honeycomb lungCongenital lung cystCongenital polycystic disease of lungCongenital polycystic lungCongenital pulmonary airway malformation type 0Congenital pulmonary airway malformation type 1Congenital pulmonary airway malformation type 2Congenital pulmonary airway malformation type 3Congenital pulmonary airway malformation type 4Congenital pulmonary airway malformationsMultiple congenital bronchogenic cysts