ICD·index Chapters ENESDE
LA30.6 category

Amelogenesis imperfecta

Definition

Amelogenesis imperfecta presents with a rare abnormal formation of the enamel or external layer of the crown of teeth. Amelogenesis imperfecta is due to the malfunction of the proteins in the enamel: ameloblastin, enamelin, tuftelin and amelogenin. People afflicted with amelogenesis imperfecta have teeth with abnormal colour: yellow, brown or grey; this disorder can afflict any number of teeth of both dentitions. The teeth have a higher risk for dental cavities and are hypersensitive to temperature changes as well as rapid attrition, excessive calculus deposition, and gingival hyperplasia.

Inclusions

  • Hypocalcified amelogenesis imperfecta
  • Hypomaturation amelogenesis imperfecta

Also indexed as

AI - [amelogenesis imperfecta]Amelogenesis imperfectaAmelogenesis imperfecta - cone rod dystrophyAmelogenesis imperfecta - gingival hyperplasiaAmelogenesis imperfecta - nephrocalcinosisHypocalcified amelogenesis imperfectaHypomaturation amelogenesis imperfectaHypomaturation hypoplastic amelogenesis imperfecta with taurodontismHypoplastic amelogenesis imperfectaJalili syndromecongenital enamel hypoplasiahereditary enamel hypoplasiahypomineralisation amelogenesis imperfectahypoplasia amelogenesis imperfecta

Nearby in Structural developmental anomalies of teeth and periodontal tissues