20Developmental anomalies Structural developmental anomalies primarily affecting one body system Structural developmental anomalies of the eye, eyelid or lacrimal apparatus LA11Structural developmental anomalies of the anterior segment of eye
LA11.2
category
Anterior segment dysgenesis
Definition A condition caused by failure of the anterior structures of the eye to correctly develop during the antenatal period. This condition may present with iris hypoplasia, irregular and misplaced pupils, hazy corneas, or attachments of the iris to the cornea.
Also indexed as
Anterior segment dysgenesis Axenfeld anomaly Axenfeld syndrome Rieger-Axenfeld anomaly
Nearby in Structural developmental anomalies of the anterior segment of eye
International Classification of Diseases, Eleventh Revision (ICD-11), World Health Organization (WHO) 2019/2021, https://icd.who.int/browse11. Licensed under Creative Commons Attribution-NoDerivatives 3.0 IGO (CC BY-ND 3.0 IGO).
Release 2026-01.
View this entity in the official WHO ICD-11 browser .
This page reproduces WHO classification content for reference. It is not
medical advice and must not be used to diagnose or treat. For coding
decisions, consult the official release and your national coding guidelines.
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