FB80.0
category
Fibrous dysplasia of bone
Definition
Fibrous dysplasia of bone is a congenital non-hereditary benign bone disease, where normal bone is replaced by a fibrous-like tissue with immature osteogenesis. Bone lesions are mono- or polyostotic and may be associated with bone pain and fragility, leading to fractures. In some patients or bone sites, they are hypertrophic, and responsible for neurological complications.
Also indexed as
Albright-McCune-Sternberg syndromeFamilial fibrous dysplasia of jawFibrous dysplasia (monostotic), acromioclavicular jointFibrous dysplasia (monostotic), ankle jointFibrous dysplasia (monostotic), ankle or footFibrous dysplasia (monostotic), buttockFibrous dysplasia (monostotic), carpusFibrous dysplasia (monostotic), clavicleFibrous dysplasia (monostotic), elbow jointFibrous dysplasia (monostotic), femurFibrous dysplasia (monostotic), fibulaFibrous dysplasia (monostotic), fingersFibrous dysplasia (monostotic), forearmFibrous dysplasia (monostotic), glenohumeral jointFibrous dysplasia (monostotic), handFibrous dysplasia (monostotic), headFibrous dysplasia (monostotic), hip (joint)Fibrous dysplasia (monostotic), humerusFibrous dysplasia (monostotic), knee jointFibrous dysplasia (monostotic), lower legFibrous dysplasia (monostotic), metacarpusFibrous dysplasia (monostotic), metatarsusFibrous dysplasia (monostotic), multiple sitesFibrous dysplasia (monostotic), neckFibrous dysplasia (monostotic), other joints in footFibrous dysplasia (monostotic), pelvic region or thighFibrous dysplasia (monostotic), pelvisFibrous dysplasia (monostotic), radiusFibrous dysplasia (monostotic), ribsFibrous dysplasia (monostotic), scapulaFibrous dysplasia (monostotic), shoulder regionFibrous dysplasia (monostotic), skullFibrous dysplasia (monostotic), sternoclavicular jointFibrous dysplasia (monostotic), tarsusFibrous dysplasia (monostotic), tibiaFibrous dysplasia (monostotic), toesFibrous dysplasia (monostotic), trunkFibrous dysplasia (monostotic), ulnaFibrous dysplasia (monostotic), upper armFibrous dysplasia (monostotic), vertebral columnFibrous dysplasia (monostotic), wrist jointFibrous dysplasia of boneFibrous dysplasia of jawFibrous dysplasia with pigmentary skin changes and precocious pubertyJaffe-Lichtenstein syndromeMazabraud syndromeMcCune-Albright syndromeMonostotic fibrous dysplasiaMonostotic fibrous dysplasia, acromioclavicular jointMonostotic fibrous dysplasia, ankle jointMonostotic fibrous dysplasia, ankle or footMonostotic fibrous dysplasia, buttockMonostotic fibrous dysplasia, carpusMonostotic fibrous dysplasia, clavicleMonostotic fibrous dysplasia, elbow jointMonostotic fibrous dysplasia, femurMonostotic fibrous dysplasia, fibulaMonostotic fibrous dysplasia, fingersMonostotic fibrous dysplasia, forearmMonostotic fibrous dysplasia, glenohumeral jointMonostotic fibrous dysplasia, handMonostotic fibrous dysplasia, headMonostotic fibrous dysplasia, hip jointMonostotic fibrous dysplasia, humerusMonostotic fibrous dysplasia, knee jointMonostotic fibrous dysplasia, lower legMonostotic fibrous dysplasia, metacarpusMonostotic fibrous dysplasia, metatarsusMonostotic fibrous dysplasia, multiple sitesMonostotic fibrous dysplasia, neckMonostotic fibrous dysplasia, other joints in footMonostotic fibrous dysplasia, pelvic region or thighMonostotic fibrous dysplasia, pelvisMonostotic fibrous dysplasia, radiusMonostotic fibrous dysplasia, ribsMonostotic fibrous dysplasia, scapulaMonostotic fibrous dysplasia, shoulder regionMonostotic fibrous dysplasia, skullMonostotic fibrous dysplasia, sternoclavicular jointMonostotic fibrous dysplasia, tarsusMonostotic fibrous dysplasia, tibiaMonostotic fibrous dysplasia, toesMonostotic fibrous dysplasia, trunkMonostotic fibrous dysplasia, ulnaMonostotic fibrous dysplasia, upper armMonostotic fibrous dysplasia, vertebral columnMonostotic fibrous dysplasia, wrist jointPFD - [polyostotic fibrous dysplasia]Polyostotic fibrous dysplasiafibrous dysplasia, site unspecifiedlocalised osteitis fibrosamonostotic dysplasiaosteitis fibrosa circumscriptaosteitis fibrosa disseminatapolyostotic fibrodysplasiapolyostotic fibrous dysplasia of bone