EC20.2
category
Hereditary acantholytic dermatoses
Definition
A group of heritable disorders characterised by epidermal acantholysis and loss of epidermal integrity.
Inclusions
- Darier disease
- Hailey-Hailey disease
Also indexed as
Acrokeratosis verruciformis of DarierBenign familial pemphigusDarier diseaseDarier disease (MIM 124200)Darier-White diseaseDyskeratosis follicularisGougerot-Hailey-Hailey diseaseHailey-Hailey diseaseHereditary acantholytic dermatosesKeratosis follicularis
Nearby in Genetic disorders of keratinisation