EA94
category
Pityriasis rubra pilaris
Definition
Pityriasis rubra pilaris (PRP) is the name given to a group of clinically similar papulosquamous dermatoses of unknown aetiology. They initially present with erythematous, hyperkeratotic perifollicular papules, which tend to coalesce into plaques, but may progress to erythroderma, particularly in adults. The distribution, age of onset and speed of onset differ markedly between patients and these differences have been used to classify PRP into a number of clinically distinct subtypes.
Also indexed as
Devergie's diseaseHIV-associated pityriasis rubra pilarisPRP - [pityriasis rubra pilaris]Pityriasis rubra pilarisPityriasis rubra pilaris type I, classical adultPityriasis rubra pilaris type II, atypical adultPityriasis rubra pilaris type III, classical juvenilePityriasis rubra pilaris type IV, circumscribed juvenilePityriasis rubra pilaris type V, atypical juvenilePityriasis rubra pilaris, adultPityriasis rubra pilaris, juvenile