Primary sclerosing cholangitis

Definition

Primary sclerosing cholangitis is a chronic disease which shows focal or multifocal strictures of intra- and/or extra-hepatic bile ducts without any apparent causes, leading to cholestasis and ultimately liver cirrhosis and liver failure.

3 subordinate codes

• DB96.20Primary sclerosing cholangitis with cirrhosis
• 4B4YOther specified diseases of the immune system
• 4B4ZDiseases of the immune system, unspecified

Nearby in Autoimmune liver disease

• DB96.0Autoimmune hepatitis
• DB96.1Primary biliary cholangitis
• 4B4YOther specified diseases of the immune system
• 4B4ZDiseases of the immune system, unspecified