BD93.0
category
Primary lymphoedema
Definition
Lymphoedema as a result of lymphatic vessel hypoplasia
Also indexed as
Complex primary lymphoedemaCongenital lymphoedemaCongenital primary lymphoedemaDeafness, lymphoedema and leukaemia syndromeEmberger syndromeHennekam lymphangiectasia-lymphoedema syndromeHennekam syndromeHereditary lymphoedema type IHereditary lymphoedema type IILDS - [lymphoedema distichiasis syndrome]Lymphoedema praecoxLymphoedema with atrial septal defects and facial changesLymphoedema, microcephaly and chorioretinopathy syndromeLymphoedema-distichiasis syndromeMeige diseaseMilroy diseasePeripubertal primary lymphoedemaPrimary lymphoedemaSimple primary lymphoedemaSporadic late-onset primary lymphoedema