8B60.3
category
Progressive muscular atrophy
Definition
In progressive muscular atrophy, lower motor neuron signs in limb and trunk muscles are present without upper motor neuron involvement. Over time, some patients may progress to develop upper motor neuron signs, of which pathological evidence is common even in patients who never displayed clinical upper motor neuron signs, suggesting that progressive muscular atrophy is a form of ALS.
Exclusions
- Amyotrophic lateral sclerosis
(8B60.0) - Fazio-Londe syndrome
(4B4Y)
Also indexed as
Duchenne-Aran atrophyDuchenne-Aran muscle atrophyPMA - [progressive muscular atrophy]Progressive muscular atrophyhereditary SMA - [spinal muscle atrophy]hereditary spinal muscle atrophyprogressive muscle atrophyprogressive spinal muscle atrophypure progressive muscular atrophy