5C90.0
category
Liver diseases due to urea cycle defects
Definition
This is a group of liver diseases due to defects in the urea cycle, which is a metabolic cycle of nitrogen-containing compounds that produces the waste product urea.
Also indexed as
Liver diseases due to urea cycle defects
Nearby in Metabolic or transporter liver disease
5C90.1Liver diseases due to disorders of porphyrin or bilirubin metabolism or transport5C90.2Liver diseases due to disorders of amino acid metabolism5C90.3Liver disease due to disorders of lysosomal storage5C90.4Liver diseases due to mitochondrial disorders5C90.5Liver diseases due to disorders of mineral metabolism4B4YOther specified diseases of the immune system4B4ZDiseases of the immune system, unspecified