ICD·index Chapters ENESDE
5C63.20 category

Hypocalcaemic vitamin D dependent rickets

Definition

Hypocalcaemic vitamin D-dependent rickets (VDDR-I) is an early-onset hereditary vitamin D metabolism disorder characterised by severe hypocalcaemia leading to osteomalacia and rachitic bone deformations, and moderate hypophosphatemia.

Also indexed as

Hypocalcaemic vitamin D dependent ricketsVitamin D-dependency type I

Nearby in Disorders of vitamin D metabolism or transport