Disorders of fructose metabolism

Definition

This refers to disorders of the metabolism of fructose in the phosphorylation of fructose to fructose 1-phosphate by fructokinase, thus trapping fructose for metabolism in the liver.

3 subordinate codes

• 5C51.50Hereditary fructose intolerance
• 4B4YOther specified diseases of the immune system
• 4B4ZDiseases of the immune system, unspecified

Nearby in Inborn errors of carbohydrate metabolism

• 5C51.0Disorders of the pentose phosphate pathway
• 5C51.1Disorders of glycerol metabolism
• 5C51.2Disorders of glyoxylate metabolism
• 5C51.3Glycogen storage disease
• 5C51.4Disorders of galactose metabolism
• 4B4YOther specified diseases of the immune system
• 4B4ZDiseases of the immune system, unspecified