5A70.0
category
Pituitary-dependent Cushing disease
Definition
Pituitary-dependent Cushing disease is caused by a pituitary tumour, generally benign (adenoma) but rarely malignant (carcinoma), which secretes adrenocorticotropin (ACTH) autonomously, leading to hypercortisolism. The condition is associated with increased morbidity and mortality that can be mitigated by treatments that result in sustained endocrine remission. Transsphenoidal pituitary surgery (TSS) remains the mainstay of treatment for this disease but requires considerable neurosurgical expertise and experience in order to optimize patient outcomes.
Also indexed as
ACTH- [adrenocorticotropic hormone] secreting pituitary adenomaCorticotroph pituitary adenomaCushing diseaseCushing syndrome or disease, pituitary-dependentCushing's diseaseCushing's syndrome 3Cushings basophilismItsenko diseaseItsenko-Cushing syndromeOverproduction of pituitary ACTHPituitary-dependent Cushing diseasePituitary-dependent hyperadrenocorticismpituitary ACTH hypersecretionpituitary basophilismpituitary-dependent hypercorticalismsuprarenogenic syndrome