04Diseases of the immune system Autoinflammatory disorders
4A61
category
SAPHO syndrome
Definition SAPHO syndrome is characterised by a constellation of symptoms and signs including synovitis, acne conglobata or fulminans, palmoplantar pustulosis, hyperostosis and osteitis. Its aetiology is poorly understood.
Also indexed as
Pustulo-psoriatic hyperostotic spondylarthritis SAPHO - [synovitis, acne, pustulosis, hyperostosis, osteitis] syndrome SAPHO syndrome
Nearby in Autoinflammatory disorders
International Classification of Diseases, Eleventh Revision (ICD-11), World Health Organization (WHO) 2019/2021, https://icd.who.int/browse11. Licensed under Creative Commons Attribution-NoDerivatives 3.0 IGO (CC BY-ND 3.0 IGO).
Release 2026-01.
View this entity in the official WHO ICD-11 browser .
This page reproduces WHO classification content for reference. It is not
medical advice and must not be used to diagnose or treat. For coding
decisions, consult the official release and your national coding guidelines.
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